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本病系指铁在肺内异常蓄积,临床反复、顽固性肺泡内出血为特点之疾病。常始于婴儿,文献报告年龄最小者仅40天,发生于成人者少见。国外至1978年报告数百例。国内1966年以前仅报告4例,近年来报告逐渐增加。我科自1958年～1979年共收治8例。由于本病比较少见,绝大部分病例于发病早期常被误诊。本病病因迄今未明,治疗困难,有必要进行研究,以探索其发病规律、诊断及治疗办法。现将本院儿科收治之病例报告如下:
The disease refers to the abnormal accumulation of iron in the lungs, clinical recurrence, intracranial alveolar hemorrhage is characterized by disease. Often began in infants, the literature reported the youngest only 40 days, occurred in adults are rare. Foreign Report to Hundreds of Cases in 1978. Only 4 cases were reported before 1966 in China, and the reports have been increasing in recent years. Our department from 1958 to 1979 were treated in 8 cases. As the disease is relatively rare, the vast majority of cases are often misdiagnosed in the early onset. The etiology of the disease so far unknown, the treatment is difficult, it is necessary to conduct research to explore its incidence, diagnosis and treatment. Now hospital cases of pediatric cases are as follows: