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本病又称皮肤粘膜色素斑—胃肠道多发性息肉综合征(Peutz-Jegher’s Syndrome)是一种先天性家族性疾病,在儿科病例中较为少见。本例男患儿,12岁,自幼体弱,消化功能及食欲欠佳。出生后,在唇、口腔粘膜处见大小不等,园或卵园形,十来个黑色素沉着斑,有增多趋势。后经手术证实,在空肠部有2×2×1.5厘米大小的息肉,并有肠套迭,病检为肠腺型息肉。在临床上如有特殊的色素斑分
The disease, also known as mucocutaneous mucosal pigmentation - gastrointestinal polyposis syndrome (Peutz-Jegher’s Syndrome) is a congenital familial disease, rare in pediatric cases. This case of male children, 12 years old, infirm, digestive function and poor appetite. After birth, in the lip, oral mucosa at the size of see, park or egg park, ten melanin spots, there is an increasing trend. After surgery confirmed in the jejunum Department of 2 × 2 × 1.5 cm in size of the polyps, and intussusception, disease detection of intestinal adenoid polyps. In clinical special pigment spots if any points