小儿进行性肌营养不良是隐性遗传性家族性疾病,最主要病理改变是随意肌肌群纤维变性被结缔组织及脂肪所取代,使病肌进行性萎缩,终至形成瘫痪。目前对其发病机理尚未得到确切答案,故尚无特效疗法,我们试用免疫抑制法治疗一例,疗效满意。患儿男,11岁,于1979年3月17日来诊。患儿从七岁时发现两下肢肌群,尤以腓肠肌局部肿大变硬,曾在某医院误为肿瘤行手术切开,术中发现,腓肠肌 Pediatric progressive muscular dystrophy is a recessive hereditary familial disease, the most important pathological changes are random muscle fibers were replaced by connective tissue and fat, so that the disease muscle progressive atrophy, and finally the formation of paralysis. At present its pathogenesis has not yet been the exact answer, so there is no effective treatment, we try a case of immunosuppressive therapy, the effect is satisfactory. Children male, 11 years old, came to the clinic on March 17, 1979. Children from the age of seven found two lower extremity muscles, especially in the gastrocnemius local enlargement harden, mistaken for a tumor in a hospital underwent surgical incision, intraoperative findings, gastrocnemius